Hemifacial Microsomia

Hemifacial Microsomia is a birth deformity affecting the bony skeleton and soft tissues of the craniofacial region. It is typically characterized by pronounced asymmetry of the face due to deficient growth of the lower jaw (mandible) on one side, deficient soft tissues of the face and underdeveloped ear (microtia).

Bony and soft tissue structures on one side of the face grow lesser than the other side. The affected side of the face appears disproportionately smaller than the other. Commonly affected are the lower jaw, eye, ear, facial nerve and cheek. The most significant of these deformities is that of the jaws, which when corrected, minimizes the entire deformity and makes the face look more symmetric.

In hemifacial microsomia, the shape and size of the lower jaw is deformed on one side causing an asymmetric face. The chin appears deviated to the affected side. Facial asymmetry progresses as the patient grows. As a result, teeth bite (occlusion) is slanted.

Treatment

Based on various parameters like severity of the defect and age of the patient, there are different treatment options. Cheek and eye socket bone defects if present, can be corrected with specialized craniofacial surgeries. Ear and soft tissue defects can be rehabilitated with reconstructive surgeries.

Distraction Osteogenesis

The goal of treatment in hemifacial microsomia is to elongate the deficient jaw bone to restore facial symmetry and correct the slanting bite (occlusion). To achieve this, an advanced and effective treatment technique is distraction osteogenesis. This is a new technique for regenerating new bone by slow, progressive stretching of the bone, without requiring a bone graft.

The jaw bone on the deficient side is cut. A sophisticated device called distractor is placed such that the two arms of the device are fixed to the two segments of jaw bone. After a few days, a screw attached to the distractor is turned gradually, ideally at a rate of 1 mm per day. When this is done, the two cut segments move apart and new bone is formed in the resultant gap. After the new bone is stabilized, the distractor device is removed.

Subsequently, the jaw bone is lengthened to the desired amount correcting the asymmetry of the face. This is a powerful tissue engineering technique for generating unlimited bone.

Eminent Facio-Maxillary Surgeon Dr. S.M. Balaji is highly acclaimed for his prowess in the treatment of Hemifacial Microsomia. He is a pioneering expert in this field and has applied several revolutionary techniques including “Simultaneous Maxillary and Mandibular Distraction” giving excellent results to set right facial asymmetry.

Our hospital has to its credit the maximum number of cases of Hemifacial Microsomia successfully treated with Distraction Osteogenesis (Distraction of both upper and lower jaw) for the correction of facial asymmetries.

CASE I:
  • Facial asymmetry in a patient with Hemifacial Microsomia

    Facial asymmetry in a patient with Hemifacial Microsomia

  •  Ear deformity in patient with hemifacial microsomia

    Ear deformity in patient with hemifacial microsomia

  • Jaw bone segmented on the left side and preparation to fix distractor device

    Jaw bone segmented on the left side and preparation to fix distractor device

  • Distractor-device-fixed-to-jaw-bone

    Distractor device fixed to jaw bone

  • Ear deformity in patient with hemifacial microsomia

    Ear deformity in patient with hemifacial microsomia

  • Jaw bone segmented on the left side and preparation to fix distractor device

    Jaw bone segmented on the left side and preparation to fix distractor device

  • Activating the distractor to lengthen the jaw bones

    Activating the distractor to lengthen the jaw bones

  • Bone segments moving apart to lengthen bone

    Bone segments moving apart to lengthen bone

  • Facial asymmetry corrected with distraction osteogenesis

    Facial asymmetry corrected with distraction osteogenesis

CASE II
  • Hemifacial Microsomia with facial asymmetry, slanting smile and chin deviation

    Hemifacial Microsomia with facial asymmetry, slanting smile and chin deviation

  • CT scan image showing asymmetry of facial skeleton

    CT scan image showing asymmetry of facial skeleton

  • Improper bile due to hemifacial microsomia

    Improper bile due to hemifacial microsomia

  • Distraction Osteogenesis treatment planning

    Distraction Osteogenesis treatment planning

  • Placing the intraoral distractor

    Placing the intraoral distractor

  • Fixing the intraoral distractor during surgery

    Fixing the intraoral distractor during surgery

  • Bite improved after treatment

    Bite improved after treatment

  • X-ray showing skeletal asymmetry of the face corrected after treatment

    X-ray showing skeletal asymmetry of the face corrected after treatment

  • Asymmetry of the face corrected with distraction osteogenesis without scars

    Asymmetry of the face corrected with distraction osteogenesis without scars/p>

CASE III
  • Asymmetrical face in a patient of hemifacial microsomia

    Asymmetrical face in a patient of hemifacial microsomia

  • CT scan image before surgery showing facial asymmetry

    CT scan image before surgery showing facial asymmetry

  • X-ray showing deficient growth of the lower jaw bone on left side

    X-ray showing deficient growth of the lower jaw bone on left side

  • X-ray at the end of distraction treatment showing corrected asymmetry

    X-ray at the end of distraction treatment showing corrected asymmetry

  • Face made more symmetrical after distraction osteogenesis

    Face made more symmetrical after distraction osteogenesis